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Anti-LMNA Monoclonal Antibody (5B815)

Synonyms: PRO1, LMNL1, LMNC, LMN1, LFP, LDP1, IDC, HGPS, FPLD2, FPLD, FPL, EMD2, CMT2B1, CMD1A, CDDC, CDCD1
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Anti-LMNA Monoclonal Antibody (5B815) 是一种 Mouse 抗体,靶向 LMNA。Anti-LMNA Monoclonal Antibody (5B815) 可用于 WB,IHC。

Anti-LMNA Monoclonal Antibody (5B815)

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Rating icon 还可以
货号 TMAT-0659

别名 PRO1, LMNL1, LMNC, LMN1, LFP, LDP1, IDC, HGPS, FPLD2, FPLD, FPL, EMD2, CMT2B1, CMD1A, CDDC, CDCD1

Anti-LMNA Monoclonal Antibody (5B815) 是一种 Mouse 抗体,靶向 LMNA。Anti-LMNA Monoclonal Antibody (5B815) 可用于 WB,IHC。

Anti-LMNA Monoclonal Antibody (5B815)
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产品介绍


生物活性
产品描述
Anti-LMNA Monoclonal Antibody (5B815) is a Mouse antibody targeting LMNA. Anti-LMNA Monoclonal Antibody (5B815) can be used in WB,IHC.
别名
PRO1, LMNL1, LMNC, LMN1, LFP, LDP1, IDC, HGPS, FPLD2, FPLD, FPL, EMD2, CMT2B1, CMD1A, CDDC, CDCD1
Ig Type
IgG1
克隆号
5B815
反应种属
Human,Mouse,Rat
应用WBIHC
推荐剂量
WB: 1/500-1/2000; IHC: 1/200-1/1000
抗体种类
Monoclonal
宿主来源Mouse
构建方式Hybridoma Monoclonal Antibody
纯化方式Purified by protein A or protein G
性状Liquid
缓冲液Ascitic fluid containing 0.03% sodium azide.
浓度1 mg/mL
研究背景The nuclear lamina consists of a two-dimensional matrix of proteins located next to the inner nuclear membrane. The lamin family of proteins make up the matrix and are highly conserved in evolution. During mitosis, the lamina matrix is reversibly disassembled as the lamin proteins are phosphorylated. Lamin proteins are thought to be involved in nuclear stability, chromatin structure and gene expression. Vertebrate lamins consist of two types, A and B. Through alternate splicing, this gene encodes three type A lamin isoforms. Mutations in this gene lead to several diseases: Emery-Dreifuss muscular dystrophy, familial partial lipodystrophy, limb girdle muscular dystrophy, dilated cardiomyopathy, Charcot-Marie-Tooth disease, and Hutchinson-Gilford progeria syndrome.
偶联与修饰
偶联
Unconjugated
抗原信息
免疫原
Purified recombinant fragment of human LMNA expressed in E. Coli.
抗原种属
Human
基因名称
LMNA
基因ID
蛋白名称
Prelamin-A/C
Uniprot ID
化学信息
分子量Theoretical: 74 kDa.
储存&溶解度
储存方式Store at -20°C or -80°C for 12 months. Avoid repeated freeze-thaw cycles.
运输方式Shipping with blue ice.

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