Anti-GNS Antibody (8J37)

Name: Anti-GNS Antibody (8J37)
Brand: TargetMol
SKU: TMAY-00606
Rating: 4.5 (1 reviews)

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产品编号 TMAY-00606

Anti-GNS Antibody (8J37) 是一种 Rabbit 抗体，靶向 GNS。Anti-GNS Antibody (8J37) 可用于 WB,ELISA。

Anti-GNS Antibody (8J37)

还可以

产品编号 TMAY-00606

Anti-GNS Antibody (8J37) 是一种 Rabbit 抗体，靶向 GNS。Anti-GNS Antibody (8J37) 可用于 WB,ELISA。

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生物活性

产品描述	Anti-GNS Antibody (8J37) is a Rabbit antibody targeting GNS. Anti-GNS Antibody (8J37) can be used in WB,ELISA.
Ig Type	Monoclonal Rabbit IgG
克隆号	8J37
交叉反应	Human
验证活性	Anti-GNS rabbit monoclonal antibody at 1:500 dilution. -Lane A: PC3 Whole Cell lysate. -Lysates/proteins at 30 μg per lane. -Secondary -Goat Anti-Rabbit IgG H&L (Dylight800) at 1/10000 dilution. -Developed using the Odyssey technique. -Performed under reducing conditions. -Predicted band size:62 kDa. -Observed band size:95 kDa
应用	WB,ELISA
推荐剂量	WB: 1:500-1:2000; ELISA: 1:5000-1:10000
抗体种类	Monoclonal
宿主来源	Rabbit
构建方式	This antibody was obtained from a rabbit immunized with purified, recombinant Human GNS / G6S (rhGNS; NP_002067.1Met 1-Leu 552).
纯化方式	Protein A
性状	Liquid
缓冲液	0.2 μm filtered solution in PBS
研究背景	Glucosamine (N-acetyl)-6-sulfatase (GNS), also known as G6S, a hydrolase, which is one of the enzymes involved in heparan sulfate catabolism leading to lysosomal storage. GNS is required for the catabolism of the glycosaminoglycans (GAG) including heparin, heparan sulfate, and keratan sulfate through the hydrolysis of the 6-sulfate group from the N-acetyl-D-glucosamine 6-sulfate units. Mucopolysaccharidosis type IIID (MPS IIID) is the least common of the four subtypes of Sanfilippo syndrome. It is caused by a deficiency of N-acetylglucosamine-6-sulphatase. A mutation in GNS resulting in MPS IIID indicates the potential utility of molecular diagnosis for this rare condition. As the least common type of the four subtypes of Sanfilippo syndrome, MPS IIID has profound mental deterioration, hyperactivity, and relatively mild somatic manifestations.

偶联与修饰

偶联	Unconjugated

抗原信息

免疫原	Recombinant Human GNS protein
抗原种属	Human

存储&运输

储存方式	Store at 2°C-8°C for 1 month. Store at -20°C or -80°C for 12 months. Avoid repeated freeze-thaw cycles. Preservative-Free.
运输方式	Shipping with blue ice.