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Anti-Dymeclin Polyclonal Antibody

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货号 TMAB-05358

Anti-Dymeclin Polyclonal Antibody 是一种 Rabbit 抗体,靶向 Dymeclin。Anti-Dymeclin Polyclonal Antibody 可用于 IHC-P,IHC-Fr,IF。

Anti-Dymeclin Polyclonal Antibody

Anti-Dymeclin Polyclonal Antibody

一键复制产品信息
Rating icon 还可以
货号 TMAB-05358

Anti-Dymeclin Polyclonal Antibody 是一种 Rabbit 抗体,靶向 Dymeclin。Anti-Dymeclin Polyclonal Antibody 可用于 IHC-P,IHC-Fr,IF。

规格价格库存数量
50 μL
¥ 1,175
5日内发货
100 μL
¥ 1,970
5日内发货
200 μL
¥ 2,780
5日内发货
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产品介绍


生物活性
产品描述
Anti-Dymeclin Polyclonal Antibody is a Rabbit antibody targeting Dymeclin. Anti-Dymeclin Polyclonal Antibody can be used in IHC-P,IHC-Fr,IF.
Ig Type
IgG
反应种属
Human,Rat (predicted:Mouse,Dog,Cow,Horse,Sheep)
应用IHC-PIHC-FrIF
推荐剂量
IHC-P: 1:100-500; IHC-Fr: 1:100-500; IF: 1:100-500
抗体种类
Polyclonal
宿主来源Rabbit
亚细胞定位Cytoplasmic and Golgi Apparatus
组织特异性Expressed in most embryo-fetal and adult tissues. Abundant in primary chondrocytes, osteoblasts, cerebellum, kidney, lung, stomach, heart, pancreas and fetal brain. Very low or no expression in the spleen, thymus, esophagus, bladder and thyroid gland.
构建方式Polyclonal Antibody
纯化方式Protein A purified
性状Liquid
缓冲液0.01M TBS (pH7.4) with 1% BSA, 0.02% Proclin300 and 50% Glycerol.
浓度1mg/ml
研究背景Dyggve-Melchior-Clausen syndrome (DMC), a rare autosomal recessive disorder, is characterized by microcephaly, short trunk dwarfism and sometime psychomotor retardation. Cutaneous cells of affected individuals show dilated rough endoplasmic reticulum and enlarged vacuoles. The Dyggve-Melchior-Clausen syndrome protein, also designated dymeclin, may play a role in proteoglycan metabolism and intracellular protein digestion. It is a widely expressed multi-pass membrane protein, detected primarily in chondrocytes and fetal brain tissue. Defects in dymeclin are also the cause of Smith-McCort dysplasis syndrome (SMC), which has characteristics identical to those of Dyggve-Melchior-Clausen syndrome.
抗原信息
免疫原
KLH conjugated synthetic peptide: human Dymeclin
抗原种属
Human
基因名称
DYM
基因ID
蛋白名称
Dymeclin
Uniprot ID
功能
Necessary for correct organization of Golgi apparatus. Involved in bone development.
化学信息
分子量Theoretical: 76 kDa.
储存&溶解度
储存方式Store at 2°C-8°C for 1 month. Store at -20°C or -80°C for 12 months. Avoid repeated freeze-thaw cycles.
运输方式Shipping with blue ice.
存储store at low temperature | -20°C for 1 year

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