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Anti-HMBS Antibody (2C30) 是一种 Rabbit 抗体,靶向 HMBS。Anti-HMBS Antibody (2C30) 可用于 WB。
Anti-HMBS Antibody (2C30) 是一种 Rabbit 抗体,靶向 HMBS。Anti-HMBS Antibody (2C30) 可用于 WB。
规格 | 价格 | 库存 | 数量 |
---|---|---|---|
50 μL | ¥ 1,495 | 5日内发货 | |
100 μL | ¥ 2,490 | 5日内发货 |
产品描述 | Anti-HMBS Antibody (2C30) is a Rabbit antibody targeting HMBS. Anti-HMBS Antibody (2C30) can be used in WB. |
别名 | UPS, Pre-Uroporphyrinogen Synthase, Porphobilinogen Deaminase, PBG-D, PBGD, Hydroxymethylbilane Synthase, HMBS |
Ig Type | IgG |
交叉反应 | Human,Mouse,Rat |
验证活性 | 1. Western blot analysis of HMBS on different lysates using anti-HMBS antibody at 1/1,000 dilution. Positive control: Lane 1: Hela, Lane 2: 293T. |
应用 | |
推荐剂量 | WB: 1:1000-2000 |
抗体种类 | Monoclonal |
宿主来源 | Rabbit |
构建方式 | Recombinant Antibody |
纯化方式 | ProA affinity purified |
性状 | Liquid |
缓冲液 | 1*TBS (pH7.4), 1%BSA, 40%Glycerol. Preservative: 0.05% Sodium Azide. |
研究背景 | PBGD (porphobilinogen deaminase), also designated hydroxymethylbilane synthase, is a cytoplasmic enzyme found in the heme synthesis pathway. PBGD belongs to the HMBS (hydroxymethylbilane synthase) family. Deficiency of PBGD causes errors in pyrrole metabolism, which in turn leads to an inherited autosomal disorder called acute intermittent porphyria (AIP). AIP is characterized by acute attacks of neurological dysfunctions with hypertension, tachycardia, peripheral neurologic disturbances, abdominal pain and excessive amounts of aminolevulinic acid and porphobilinogen in the urine. |
偶联 | Unconjugated |
免疫原 | Recombinant Protein |
Uniprot ID |
分子量 | Theoretical: 40 kDa. |
储存方式 | Store at -20°C or -80°C for 12 months. Avoid repeated freeze-thaw cycles. |
运输方式 | Shipping with blue ice. |
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