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顶部产品介绍抗原信息化学信息储存和溶解信息计算器

Anti-BSCL2 Polyclonal Antibody

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货号 TMAB-03234

Anti-BSCL2 Polyclonal Antibody 是一种 Rabbit 抗体，靶向 BSCL2。Anti-BSCL2 Polyclonal Antibody 可用于 IHC-P,IHC-Fr,IF。

Anti-BSCL2 Polyclonal Antibody

Anti-BSCL2 Polyclonal Antibody

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Rating icon 还可以
货号 TMAB-03234

Anti-BSCL2 Polyclonal Antibody 是一种 Rabbit 抗体，靶向 BSCL2。Anti-BSCL2 Polyclonal Antibody 可用于 IHC-P,IHC-Fr,IF。

规格价格库存数量
50 μL
¥ 1,175
5日内发货
100 μL
¥ 1,970
5日内发货
200 μL
¥ 2,790
5日内发货
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产品介绍

生物活性
产品描述
Anti-BSCL2 Polyclonal Antibody is a Rabbit antibody targeting BSCL2. Anti-BSCL2 Polyclonal Antibody can be used in IHC-P,IHC-Fr,IF.
Ig Type
IgG
反应种属
Rat (predicted:Human,Mouse,Dog,Cow,Horse,Rabbit)
应用IHC-PIHC-FrIF
推荐剂量
IHC-P: 1:100-500; IHC-Fr: 1:100-500; IF: 1:100-500
抗体种类
Polyclonal
宿主来源Rabbit
组织特异性Highest expression in brain and testis.
构建方式Hybridoma Polyclonal Antibody
纯化方式Protein A purified
性状Liquid
缓冲液0.01M TBS (pH7.4) with 1% BSA, 0.02% Proclin300 and 50% Glycerol.
浓度1mg/ml
研究背景Defects in BSCL2 are the cause of congenital generalized lipodystrophy type 2 (CGL2) . Congenital generalized lipodystrophy is an autosomal recessive disorder characterized by a near absence of adipose tissue, extreme insulin resistance, hypertriglyceridemia, hepatic steatosis and early onset of diabetes. Defects in BSCL2 are the cause of spastic paraplegia type 17 (SPG17) ; also known as Silver spastic paraplegia syndrome. Spastic paraplegia is a neurodegenerative disorder characterized by a slow, gradual, progressive weakness and spasticity of the lower limbs. SPG17 is characterized by prominent amyotrophy of the hand muscles, the presence of mild to severe pyramidal tract signs, and spastic paraplegia. SPG17 is a motor neuron disease overlapping with distal spinal muscular atrophy type 5. Defects in BSCL2 are a cause of distal hereditary motor neuropathy type 5 (HMN5); also known aS distal hereditary motor neuropathy type V (DSMAV). HMN5 is an autosomal dominant disorder characterized by degeneration of motor nerve fibers, predominantly in limb distal regions.
抗原信息
免疫原
KLH conjugated synthetic peptide: human BSCL2/SPG17
抗原种属
Human
基因名称
BSCL2
基因ID
26580
蛋白名称
Seipin
功能
Endoplasmic reticulum membrane; Multi-pass membrane protein.
化学信息
分子量Theoretical: 44 kDa.
储存&溶解度
储存方式Store at 2°C-8°C for 1 month. Store at -20°C or -80°C for 12 months. Avoid repeated freeze-thaw cycles.
运输方式Shipping with blue ice.
存储store at low temperature | -20°C for 1 year

计算器

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