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Anti-SDHA Antibody (3B765)

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货号 TMAB-12603

Anti-SDHA Antibody (3B765) 是一种 Rabbit 抗体,靶向 SDHA。Anti-SDHA Antibody (3B765) 可用于 WB,IHC-P,IHC-Fr,ICC/IF,IF,IP,FCM。

Anti-SDHA Antibody (3B765)

Anti-SDHA Antibody (3B765)

一键复制产品信息
Rating icon 还可以
货号 TMAB-12603

Anti-SDHA Antibody (3B765) 是一种 Rabbit 抗体,靶向 SDHA。Anti-SDHA Antibody (3B765) 可用于 WB,IHC-P,IHC-Fr,ICC/IF,IF,IP,FCM。

规格价格库存数量
25 μL
¥ 790
5日内发货
50 μL
¥ 1,380
5日内发货
100 μL
¥ 2,485
5日内发货
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产品介绍


生物活性
产品描述
Anti-SDHA Antibody (3B765) is a Rabbit antibody targeting SDHA. Anti-SDHA Antibody (3B765) can be used in WB,IHC-P,IHC-Fr,ICC/IF,IF,IP,FCM.
Ig Type
IgG
克隆号
3B765
反应种属
Human,Mouse,Rat
应用WBIHC-PIHC-FrICC/IFIFIPFCM
推荐剂量
WB: 1:500-2000; IHC-P: 1:50-200; IHC-Fr: 1:50-200; ICC/IF: 1:50-200; IF: 1:50-200; IP: 1:20-50; FCM: 1:50-100
抗体种类
Monoclonal
宿主来源Rabbit
构建方式Recombinant Antibody
纯化方式Protein A purified
性状Liquid
缓冲液10mM phosphate buffered saline (pH 7.4) with 150mM sodium chloride, 0.05% BSA, 0.02% Proclin300 and 50% glycerol.
研究背景Flavoprotein (FP) subunit of succinate dehydrogenase (SDH) that is involved in complex II of the mitochondrial electron transport chain and is responsible for transferring electrons from succinate to ubiquinone.
抗原信息
免疫原
A synthesized peptide: human SDHA
抗原种属
Human
基因名称
SDHA
基因ID
蛋白名称
Succinate dehydrogenase [ubiquinone] flavoprotein subunit, mitochondrial
Uniprot ID
功能
Defects in SDHA are a cause of mitochondrial complex II deficiency (MT-C2D). A disorder of the mitochondrial respiratory chain with heterogeneous clinical manifestations. Clinical features include psychomotor regression in infants, poor growth with lack of speech development, severe spastic quadriplegia, dystonia, progressive leukoencephalopathy, muscle weakness, exercise intolerance, cardiomyopathy. Some patients manifest Leigh syndrome or Kearns-Sayre syndrome.
化学信息
分子量Theoretical: 73 kDa. Actual: 72 kDa.
储存&溶解度
储存方式Store at 2°C-8°C for 1 month. Store at -20°C or -80°C for 12 months. Avoid repeated freeze-thaw cycles.
运输方式Shipping with blue ice.
存储store at low temperature | -20°C for 1 year

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